Abstract: Sj?gren’s syndrome（SS） is a idiopathic systemic autoimmune disease affecting the exocrine glands and extraglandular organs with an increased incidence of lymphoma. The occurrence of SS is rare in childhood .The clinical presentation of childhood Sj?gren’s syndrome may differ from the clinical presentation in adulthood，which could be most likely to be misdiagnosed or delayed in diagnosis. With increasing researches and deeper understanding of the disease，the classification criteria for adult SS are constantly being adjusted and revised. No specific diagnosis criteria have been established for SS in childhood. This paper reviews and evaluates several classification criteria of adult SS and the proposals for diagnosis criteria for childhood SS in order to provide help for the early diagnosis and related researches of childhood SS.

Key words: Sj?gren’s syndrome, classification criteria, diagnosis, child

摘要： 干燥综合征是一种累及外分泌腺体和腺体外器官、同时伴有淋巴瘤发生率增高的特异性系统性自身免疫性疾病。该病多见于成人，儿童罕见。儿童干燥综合征的临床特征与成人有所不同，经常被误诊或诊断延迟。随着对本病的研究和认识的深入，成人干燥综合征分类标准在不断进行调整和修订，然而至今没有制定出针对儿童干燥综合征的诊断标准。文章回顾分析了有关成人干燥综合征分类标准和儿童原发性干燥综合征诊断标准的建议，以期对儿童干燥综合征的早期诊断和相关研究提供帮助。

关键词: 干燥综合征, 分类标准, 诊断, 儿童