Malignant change of congenital biliary dilatation and its treatment        CHEN Yan-ling, HAN Sheng-hua. Department of Hepatobiliary Surgery, Union Hospital, Fujian Medical University, Fuzhou 350001, China
Corresponding author: CHEN Yan-ling, E-mail：ylchen@medmail.com.cn
Abstract    Congenital biliary dilatation (CBD) is a premalignant lesion. Pancreaticobiliary maljunction plays important roles in the process of malignant change. The incidence of malignant change increases obviously with age．Complete cyst excision with cholecystectomy and Roux-en-Y hepaticojejunostomy is required as soon as a diagnosis is made to interrupt the cancerous potential. The clinical symptom of malignant change of CBD is  nonspecific．Preoperative diagnosis is difficult and the prognosis is poor．The intraoperative frozen section should be performed to rule out the presence of cancer. The operation for carcinoma of the bile duct should be performed in CBD with malignant change. Palliative surgery should be considered to relieve symptom and improve survival in patients with unresectable disease.