Ⅲ型先天性胆管扩张症是一种少见的胆道缺陷性疾病，也称胆总管开口囊性脱垂、胆总管末端囊肿或胆总管膨出。内镜超声、磁共振胰胆管成像（MRCP）、内镜下逆行胰胆管造影术（ERCP）对诊断该病具有极其重要的作用。由于该病恶变率低，内镜下囊肿开窗引流和（或）Oddi括约肌切开术是该病的首选方法。

Diagnosis and treatment of Type Ⅲ congenital biliary dilatation        WU Zhi-yong, CHEN Wei. Department of General Surgery, Renji Hospital, Shanghai Jiaotong University School of Medicine, Shanghai 200127, China
Corresponding author: WU Zhi-yong, E-mail:zhiyongwu@gmail.com
Abstract    Type Ⅲ congenital biliary dilatation (CBD) is a rare type of biliary malformation disease. It is also called cyst prolapse of the terminal common bile duct, cyst of terminal choledochus or choledochocele. Endoscopic ultrasonogram, magnetic resonance cholangiopacreatography (MRCP) and endoscopic retrograde cholangiopancreatography (ERCP) are very important for the diagnosis. It is recommended that endoscopic unroofing and/or sphincterotomy is the first therapeutic method because of low-risk for malignancy.