Abstract: Systemic juvenile idiopathic arthritis is one of the most common rheumatic diseases in children. Interstitial lung disease is characterized by interstitial and distal air gap remodeling，which leads to abnormal gas exchange. In recent years，there are increasing reports on systemic juvenile idiopathic arthritis combined with interstitial lung disease at home and abroad. The paper summarizes the recent reports on sJIA with interstitial lung disease，and summarizes the clinical manifestations，imaging manifestations，diagnosis as well as treatment for pulmonary interstitial disease in children，in order to have a deeper understanding of this kind of disease，and contribute to the early diagnosis and treatment of pulmonary interstitial disease.

Key words: systemic juvenile idiopathic arthritis, interstitial lung disease, child

摘要： 全身型幼年特发性关节炎是儿童常见的风湿性疾病之一， 肺间质病变是指以肺间质和远端气隙重构为特征， 进而导致异常气体交换的疾病。近年来， 国内外对全身型幼年特发性关节炎合并肺间质病变的报道有增多趋势。该文总结了近年来报道中全身型幼年特发性关节炎儿童合并肺间质病变的情况， 并对儿童肺间质病变的临床表现， 影像学表现， 诊断和治疗进行综述，旨在对该类疾病有更深刻的认识， 有助于肺间质病变的早期诊治。

关键词: 幼年特发性关节炎, 全身型, 肺间质病变, 儿童