Abstract:

Hypertrophic cardiomyopathy（HCM） is a common cause of sudden deaths in children and adolescents，mostly due to ventricular arrhythmia. The abnormal ECG activity of HCM is related to the histological characteristics of myocardial hypertrophy. Although ECG lacks specificity，some changes still have certain sensitivity in HCM，or give hints to potential causes. These can provide valuable basis for the early diagnosis，as well as the monitoring and management of high-risk patients，and help estimate the time of ICD treatment.

Key words: hypertrophic cardiomyopathy, electrocardiogram abnormality, child

摘要：

肥厚型心肌病（HCM）是儿童和青少年猝死的常见原因之一， 儿童期猝死事件主要归因于室性心律失常。HCM的心电活动异常与其心肌肥厚的组织学特点和遗传性病因相关， 虽然心电异常缺乏特异性， 但某些异常对预测心电不良事件具有一定的敏感性， 或可提示潜在病因，可以为儿童HCM的病因诊断和高危患者的筛查及管理、 植入式心律转复除颤器治疗指征的把握提供有价值的依据。

关键词: 肥厚型心肌病, 心电异常, 儿童