关键词: 先天性肺血管异常, 分类, 临床表现, 诊断, 治疗

Abstract: Congenital pulmonary vascular disease are a group of diseases，which are caused by deformity of the anatomical morphology and structure of pulmonary arteries，pulmonary veins，and pulmonary vascular plexus during the embryonic development. In recent years，there have been increasing reports of such diseases. However，there is no comprehensive and systematic classification of congenital pulmonary vascular disease，which leads to confusion in the clinical diagnosis and treatment. This article summarizes the classification，clinical manifestations，diagnostic methods and treatment strategies of congenital pulmonary vascular disease.

Key words: congenital pulmonary vascular abnormality, classification, clinical manifestation, diagnosis, therapy