Objective To explore the clinical characteristics and outcomes of autoimmune pancreatitis（AIP）in children， and to provide ideas for clinical diagnosis and treatment. Methods Clinical data of 5 children diagnosed with AIP at Beijing Children’s Hospital from July 2020 to January 2024 were retrospectively analyzed.The clinical symptoms，treatment methods and follow-up results were analyzed. Results Among the 5 children with AIP ， there were 2 cases of type 2 AIP，2 cases were not specified and 1 case might be type 3 AIP.There were 4 boys and 1 girl，with an average age of（10.87±3.86）years.The main clinical manifestations were abdominal pain（4 cases）and jaundice（3 cases）. All patients had normal serum IgG4 levels.All children had typical imaging manifestations，including focal pancreatic enlargement in 4 cases and diffuse pancreatic enlargement in 1 case，with 1 case also having a focal pancreatic mass. One child underwent a pathological biopsy，which showed periductal lymphocyte infiltration and interstitial inflammatory changes in the pancreas.All 5 children achieved clinical and imaging remission after hormone treatment. No recurrence was observed during follow-up. Conclusion The incidence of AIP in children is low， the clinical features are not obvious， and the hormone therapy has significant effect. A full understanding of the clinical features of AIP in children is helpful for early identification of AIP and avoiding missed diagnosis and misdiagnosis.

autoimmune pancreatitis, child, classification, hormone

目的 探讨儿童自身免疫性胰腺炎（AIP）临床特征与转归，为临床诊治提供思路。方法　回顾性分析2020年7月至2024年1月首都医科大学附属北京儿童医院诊断的5例 AIP 患儿临床资料，分析其临床症状、治疗方法和随访结果。结果 5例中2例为2型 AIP，2例未明确分型，1例3型 AIP。其中男4例、女1例，平均年龄为（10.87±3.86）岁。临床表现主要为腹痛4例，黄疸3例。5例患儿血清 IgG4水平正常。所有患儿均有典型影像学表现，胰腺局灶性增大4例、胰腺弥漫性增大1例，其中1例同时合并胰腺局灶肿物。1例患儿进行了病理活检提示胰腺导管周围淋巴细胞浸润、胰腺间质炎性改变。5例患儿接受激素治疗后均获得临床及影像学缓解，随诊均未见复发。结论 儿童 AIP 发病率低，临床特征不明显，激素治疗效果明显；充分认识儿童 AIP 的临床特征有助于早期识别 AIP、避免漏诊及误诊。

自身免疫性胰腺炎, 儿童, 分型, 激素