关键词: 左旋肉碱, 缺乏, 疾病

Abstract: As an indispensable component in the human body，L-carnitine has important physiological functions and plays an important role in mitochondrial processes，fatty acid metabolism and ATP production. In the state of deficiency，mitochondrial function is damaged，cell metabolism is changed，and the functions of multiple systems in the body are affected，which in turn leads to the emergence of its various diseases. Exogenous L-carnitine supplementation can not only relieve metabolic disorders and disease state related to carnitine deficiency，but also help the body restore carnitine balance and maintain metabolism，energy balance and health. This article summarizes the use of L-carnitine in various diseases by reviewing the previous literature，in order to improve clinicians' understanding of L-carnitine.

Key words: L-carnitine, deficiency, disease