Abstract: The temporomandibular joint is located in the temporomandibular joint region at the lateral skull base，adjacent to the external auditory canal，and performs functions such as opening and closing the mouth，chewing，and pronunciation. Tumors and tumor-like diseases involving the temporomandibular joint and skull base are relatively rare and the location is deep. Some invasive diseases（such as synovial chondroma，temporal bone giant cell tumor，tenosynovial giant cell tumor，etc.）may invade the middle cranial fossa and middle ear，which are difficult to diagnose and treat. This article reviewed the progress in the diagnosis and treatment of tumors and tumor-like diseases involving the temporomandibular joint and skull base，and provided a theoretical basis for clinical doctors in the diagnosis and treatment of these kinds of diseases.

Key words: temporomandibular joint, tumors and tumor-like diseases, skull base

摘要： 颞下颌关节位于侧颅底的颞下颌关节区，紧邻外耳道，行使张闭口、咀嚼、发音等功能。累及颞下颌关节和颅底的肿瘤与类肿瘤病变比较少见，且位置较深，部分具有侵袭性的病变（如滑膜软骨瘤、颞骨巨细胞瘤、腱鞘巨细胞瘤等）会累及颅中窝和中耳，诊治难度较大。文章就累及颞下颌关节和颅底的肿瘤与类肿瘤病变诊治进展做一综述，为临床医生诊治此类疾病时提供理论依据。

关键词: 颞下颌关节, 肿瘤与类肿瘤病变, 颅底