关键词: 主动脉病变, 主动脉扩张, 主动脉夹层, 马凡综合征, 洛伊 - 迪茨综合征, 埃勒斯 - 当洛综合征, 遗传性胸主动脉病变, 先天性心脏病, 指南

Abstract: Pediatric aortopathy has complex etiologies，with different natural disease course and management needs from those of adults. The 2024 scientific statement from the American Heart Association proposes a standardized management framework encompassing imaging assessment，follow-up strategies，pharmacological therapy，and surgical indications. This article reviews the key management principles outlined in the statement and explores the management strategies suitable for China based on the current status of our country，aiming to increase rate of early detection，enhance risk assessment accuracy，and improve long-term outcomes.

Key words: aortopathy, aortic dilation, aortic dissection, Marfan syndrome, Loeys-Dietz syndrome, Ehlers-Danlos syndrome, inheritable thoracic aortic diseases, congenital heart disease, guidelines