中国实用儿科杂志

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儿童炎症性肌病的临床诊断思路

熊晖   

  1. 作者单位:北京大学第一医院儿科,北京 100034
  • 出版日期:2014-02-06 发布日期:2014-01-22

Clinical lines of thinking about inflammatory myopathies in children.       

XIONG Hui.   

  1. Pediatric Department of Paediatrics,Peking University First Hospital,Beijing 100034, China.
  • Online:2014-02-06 Published:2014-01-22

摘要:

儿童炎症性肌病分为自身免疫性肌炎和感染性肌炎。自身免疫性肌炎一般称为特发性炎症性肌病。儿童炎症性肌病临床诊断主要依靠临床表现、血清肌酸激酶和肌电图检查结果,病理检查可进一步确定诊断,而进行血清抗体检查对于治疗和预后判断有一定的帮助。传统的儿童皮肌炎诊断标准延用1975年Bohan和Peter标准。

关键词: 炎症性肌病, 儿童, 皮肌炎, 诊断与鉴别诊断

Abstract:

Children inflammatory myopathies are divided into autoimmunemyositises and infective myositises. Autoimmune myositises usually are called idiopathic inflammatory myopathies. Clinical diagnosis of pediatric inflammatory myopathy mainly depends on the clinical manifestation, serum creatine kinase and EMG examination, pathological examination can be further confirmed the diagnosis,the serum antibody examination will be helpful for the treatment and prognosis. The traditional JDM diagnostic criteria is Bohan and Peter standard in 1975.
Keywords: idiopathic inflammatory myopathies;children;dermatomyositis;diagnosis and differential diagnosis

Key words: idiopathic inflammatory myopathies, children, dermatomyositis, diagnosis and differential diagnosis

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