Abstract:

This article mainly introduces the pathogenesis，oral and systemic clinical manifestations，diagnosis，clinical and oral management of glycogen storage disease Ⅰb，in order to provide clinical philosophy of relevant diseases for dentists.

Key words: glycogen storage disease Ⅰb, neutropenia, periodontal disease

摘要：

文章就与牙周相关的糖原贮积病研究进展做一介绍，即糖原贮积病Ⅰb型的发病机制、口腔与全身临床表现、诊断、临床管理及口腔管理，以期为口腔临床医生提供相关罕见疾病的诊疗思路。

关键词: 糖原贮积病Ⅰb型, 中性粒细胞减少症, 牙周疾病