Abstract: Beh?et syndrome（BS） is a relatively rare，chronic and systemic vascular inflammatory disease，mainly manifested as recurrent oral ulcers，genital ulcers，cutaneous and ocular damage. This article will comprehensively discuss BS in its pathogenesis，clinical manifestations，auxiliary examination，diagnosis and differential diagnosis，therapies and prognosis.

Key words: Beh?et syndrome, vasculitis, oral ulcer, genital ulcer, uveitis

摘要： 白塞病 （Beh?et syndrome，BS）是一种少见的慢性全身性血管炎症性疾病，主要表现为复发性口腔溃疡、生殖器溃疡、皮肤及眼部损害。文章结合国内外相关指南，全面论述BS的发病机制、临床表现、诊断及鉴别诊断、治疗推荐及预后。

关键词: 白塞病, 血管炎, 口腔溃疡, 生殖器溃疡, 葡萄膜炎