关键词: 幼年特发性关节炎, 全身型, 肺间质病变, 儿童

Abstract: Systemic juvenile idiopathic arthritis is one of the most common rheumatic diseases in children. Interstitial lung disease is characterized by interstitial and distal air gap remodeling，which leads to abnormal gas exchange. In recent years，there are increasing reports on systemic juvenile idiopathic arthritis combined with interstitial lung disease at home and abroad. The paper summarizes the recent reports on sJIA with interstitial lung disease，and summarizes the clinical manifestations，imaging manifestations，diagnosis as well as treatment for pulmonary interstitial disease in children，in order to have a deeper understanding of this kind of disease，and contribute to the early diagnosis and treatment of pulmonary interstitial disease.

Key words: systemic juvenile idiopathic arthritis, interstitial lung disease, child