中国实用外科杂志 ›› 2008, Vol. 28 ›› Issue (07): 556-558.

• 论著 • 上一篇    下一篇

肝脏血管周上皮样细胞瘤1例报告并文献复习

韩威蒋伟李建设张忠涛王宇   

  1. 首都医科大学附属北京友谊医院普外科,北京100050
  • 收稿日期:2008-02-01 修回日期:2008-04-06 出版日期:2008-06-24 发布日期:2008-06-24
  • 通讯作者: 张忠涛

Perivascular epithelioid cell tumor of the liver:a report of one case and review of the literature

<a href="https://www.zgsyz.com/zgsywk/EN/article/advancedSearchResult.do?searchSQL=(((HAN Wei[Author]) AND 1[Journal]) AND year[Order])" target="_blank">HAN Wei</a>,<a href="https://www.zgsyz.com/zgsywk/EN/article/advancedSearchResult.do?searchSQL=(((JIANG Wei[Author]) AND 1[Journal]) AND year[Order])" target="_blank">JIANG Wei</a>,<a href="https://www.zgsyz.com/zgsywk/EN/article/advancedSearchResult.do?searchSQL=(((LI Jian-he[Author]) AND 1[Journal]) AND year[Order])" target="_blank">LI Jian-he</a>,<a href="https://www.zgsyz.com/zgsywk/EN/article/advancedSearchResult.do?searchSQL=(((et al.[Author]) AND 1[Journal]) AND year[Order])" target="_blank">et al.</a>   

  1. Department of General Surgery,Beijing Friendship Hospital Affiliated to Capital University of Medical Science,Beijing 100050,China
  • Received:2008-02-01 Revised:2008-04-06 Online:2008-06-24 Published:2008-06-24
  • Contact: ZHANG Zhong-tao

摘要:

目的:分析肝脏血管周上皮样细胞瘤的临床特点。方法:2007年10月首都医科大学附属北京友谊医院普外科诊治1例肝脏血管周上皮样细胞瘤,对其临床、影像、病理学特点进行分析及相关文献复习。结果:肝脏血管周上皮样细胞瘤无临床症状,无特征性影像学表现,术前难于确诊。组织学上由单一上皮样细胞构成,不含血管及脂肪成分,免疫组化呈特征性黑色素生成(HMB-45)阳性。目前文献报道肝脏血管周上皮样细胞瘤发生在肝脏者尚不足10例。结论:肝脏血管周上皮样细胞瘤是一种非常罕见的间叶组织来源肿瘤。主要依靠病理进行诊断。肝脏血管周上皮样细胞瘤生物学行为不确定,建议术后长期随访。

关键词: 肝脏, 血管周上皮样细胞瘤

Abstract:

Objective:o report a case of perivascular epithelioid cell tumor (PEComa) of the liver,and improve the understanding of the tumor. Methods:he clinical,imaging and pathological features of one case of liver perivascular epithelioid cell tumor admitted in October 2007 in Beijing Friendship Hospital Affiliated to Capital University of Medical Scienc was analyzed retrospectively and related literatures were reviewed. Results:he PEComa of liver didn't have any symptoms and characterized imaging features,and was difficult to make correct diagnosis before operation.Histologically,the resected tumor was composed of epithelioid cells,without vascular or lipomatous component,and was characterized by HMB45 positive on immunohistochemistry.Among present literatures,less than 10 cases of PEComa of the liver were reported. Conclusion:EComa is a very rare tumor of the liver which arises from mesenchymal tissues.The diagnosis of PEComa mainly depends on the pathological features.In respect of uncertain biologic potential of PEComa,long term follow up is indicated.

Key words: liver, perivascular epithelioid cell tumor