中国实用儿科杂志

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不明原因婴幼儿肺间质疾病

尚云晓冯雍   

  1. 作者单位: 中国医科大学附属盛京医院小儿呼吸内科, 辽宁 沈阳 110004
  • 出版日期:2014-12-06 发布日期:2014-12-08

Interstitial lung disease in infants of undefined etiology

SHANG Yun-xiaoFENG Yong.   

  1. Department of Pediatric Pulmonology, Shengjing Hospital of China Medical University, Shenyang 110004, China
  • Online:2014-12-06 Published:2014-12-08

摘要:

儿童肺间质疾病属少见疑难病,早期诊断、早期治疗可改善不良预后。婴幼儿时期是儿童肺间质疾病的高发阶段。近10年来,基于临床-影像学-病理学的诊断模式,确切诊断的病例逐渐增多,但仍有很多病因不明。本文就不明原因婴幼儿肺间质疾病进行阐述,以有助于临床医生对该病早期识别及诊治。

关键词: 肺间质疾病, 婴幼儿, 病因, 肺间质糖原累积症, 神经内分泌细胞增生症

Abstract:

Abstract: Children’s interstitial lung disease is a group of relatively rare and complicated pulmonary disorders,which is more prevalent in infancy periods. Early diagnosis and treatment may alter the poor prognosis. In the last ten years, with the application of clinical-radiologic-pathologic diagnosis mode, more and more interstitial lung disease can be diagnosed with a known etiology in infants, but some of them are still lack of a defined etiology. This article describes the interstitial lung disease in infants of undefined etiology,which in turn can lead to better understanding and optimal patient management.

Key words: interstitial lung disease, infant, etiology, pulmonary interstitial glycogenosis, neuroendocrine cell hyperplasia

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