Abstract: The anatomy of pulmonary atresia with intact ventricular septum（PA/IVS） varies greatly，and the choice of treatment and prognosis vary greatly. Transcatheter interventional therapy has become an important program for neonatal intervention in PA/IVS. Limited by equipment and experience，the development of interventional therapy for PA/IVS in our country is far from enough. In the article the progress of interventional therapy for neonatal PA/IVS at home and abroad was summarized，in order to provide reference schemes and ideas for improving the level of interventional therapy for neonatal PA/IVS in our country. With the development of interventional technology and materials and the continuous accumulation of clinical experience in interventional surgery，it is believed that interventional therapy for neonatal PA/IVS will be further promoted and developed.

Key words: pulmonary atresia with intact ventricular septum, newborn, interventional therapy

摘要： 室间隔完整型肺动脉闭锁（PA/IVS）解剖差异大，治疗术式的选择及预后有很大的个体化差异。经导管介入治疗已成为PA/IVS新生儿期干预的重要方案。受到设备和经验等因素制约，我国PA/IVS介入治疗开展力度远远不够。该文总结国内外及笔者团队新生儿PA/IVS的介入治疗进展，为提高我国新生儿PA/IVS的介入治疗水平提供参考方案和思路。随着介入技术和材料的发展以及介入手术临床经验的不断积累，相信新生儿PA/IVS介入治疗将会得到进一步推广及发展。

关键词: 室间隔完整型肺动脉闭锁, 新生儿, 介入治疗