Abstract:

Abstract：Long QT syndrome (LQTS) is major risk factor inducing the child and youth sudden death.Its phenotype is classified according to genotype .Now，it has been established the 13 autosomal dominant genetic types and two autosomal recessive genetic types，the most common clinical is LQT1，LQT2 and LQT3.Different subtype of LQTS has different inducing factor for malignant ventricular arrhythmia，different ECG findings，different risk stratification，different prognosis and different clinical treatment strategies.

Key words: long QT syndrome, ECG finding, risk stratificatio

摘要：

摘要：长QT综合征(long QT syndrome，LQTS)临床分型主要根据基因型进行。目前已确立了13个常染色体显性遗传基因型和2个常染色体隐性遗传基因型，临床最为常见的是LQT1、LQT2和LQT3。亚型不同恶性室性心律失常诱发因素不同，心电图表现不同，危险分层不同，预后不同，临床治疗策略不同。

关键词: 长QT综合征, 心电图, 危险分层